female pseudohermaphroditism
Female pseudohermaphroditism (FPH) is a form of disorder of gender development.
Pathology
Patients with female pseudohermaphroditism have female internal genitalia and female karyotype (46 XX) with various degree of external genitalia virilization.
Causes
- congenital adrenal hyperplasia (CAH) : considered most common cause
- transplacental androgen exposure
- XX male syndrome
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