Shy-Drager syndrome

The Shy-Drager syndrome is a neurodegenerative disease, and one of the manifestations of multiple systemic atrophy (MSA).

Terminology

It is important to note that the current belief that olivopontocerebellar degeneration, Shy-Drager syndrome and striatonigral degeneration are different manifestations of the same underlying disease, namely multiple systemic atrophy (MSA), is recent, and as such many older publications will describe these as separate entities .

For a discussion of epidemiology and pathology, please refer to multiple systemic atrophy (MSA).

Clinical presentation

The principle clinical finding in Shy-Drager syndrome is arterial orthostatic hypotension. Other autonomic signs caused by degeneration of brainstem reticular formation nuclei are also present.

Siehe auch:

• Multisystematrophie
• striatonigral degeneration
• olivopontocerebellar degeneration
• neurodegenerative Erkrankung

und weiter:

• bilateral middle cerebellar peduncle lesions
• Olivopontozerebelläre Atrophie
• orthostatische Dysregulation