Idiopathic dilatation of the pulmonary trunk

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Idiopathic dilatation of the pulmonary trunk is a rare congenital anomaly comprising pulmonary trunk enlargement with or without dilatation of the right and left pulmonary arteries.

For this diagnosis, exclusion of pulmonary and cardiac diseases (mainly pulmonary valve stenosis) and confirmation of the presence of normal pressures in the right ventricle and pulmonary artery is required. The few available reports based on the results of long-term follow-up studies indicate that this condition is benign and non-progressive.

Differential diagnosis

See also