Box-shaped heart

Radiopaedia • CC-by-nc-sa 3.0 • de

A box-shaped heart is a radiographic description given to the cardiac silhouette in some cases of Ebstein anomaly. The classic appearance of this finding is caused by the combination of the following features:

huge right atrium that may fill the entire right hemithorax
shelved appearance of the left cardiac contour due to the dilated right ventricular outflow tract or elevated residual right ventricle
small aorta and main pulmonary artery