congenital cystic eyeball

Congenital

cystic eye associated with a low-grade cerebellar lesion that spontaneously regressed. Pre-operative (A-C) and post-operative (D-F )orbit MRI study. Coronal T2w images (A-B) show a complex mass in the upper-outer and anterior portions of the left orbit with a predominantly extraconal engagement. The mass consists of a well-defined anterior cystic component (white arrow) with signal intensity similar to vitreous/cerebrospinal fluid (CSF) and a posterior component more hyperintense than the muscle signal. No normal orbital contents such as extra-ocular muscles or globe can be identified in the anterior portions of the orbit. Axial post-gadolinium fat saturated T1w image (C) shows heterogeneous enhancement of the posterior soft tissue mass. No normal orbital contents such as extraocular muscles or globe can be identified in the anterior portions of the orbit. Notice the bone defect of the lateral wall of the orbit (A, arrowhead) and the left optic nerve atrophy (C, arrowhead). Post-operative Coronal T2w MRI images (D-E) disclose a partial reduction of the complex mass in the left orbit; following gadolinium administration, the residual lesion shows a dyshomogeneous enhancement (axial post-gadolinium fat saturated T1w image, F); notice the presence of a left ocular prosthesis (F, white arrow).