Diffuse pulmonary lymphangiomatosis
Diffuse pulmonary lymphangiomatosis (DPL) is a rare condition characterized by diffuse proliferation of anastomosing lymphatic channels (lymphangiomas).
There is no recognized gender predilection. It typically manifests in children and young adults.
Described features include
- increased interlobular septal thickening
- peribronchovascular thickening
- patchy ground glass opacities
- pleural thickening
- pleural effusion
- mediastinal soft tissue infiltration