Diffuse pulmonary lymphangiomatosis
Diffuse pulmonary lymphangiomatosis (DPL) is a rare condition characterized by diffuse proliferation of anastomosing lymphatic channels (lymphangiomas).
Epidemiology
There is no recognized gender predilection. It typically manifests in children and young adults.
Radiographic features
CT chest
Described features include
- increased interlobular septal thickening
- peribronchovascular thickening
- patchy ground glass opacities
- pleural thickening
- pleural effusion
- mediastinal soft tissue infiltration
See also
