muskuloskelettale Komplikationen der Hämophilie

Teenager with

bilateral knee pain. AP (above) and lateral (below) radiographs of the knees show knee joint capsular distension due to dense effusions (left > right), periarticular osteopenia, joint space narrowing, subchondral cysts and epiphyseal overgrowth.The diagnosis was hemophilia.

Haemophilic

pseudotumour. There is a expansible lesion with well-defined borders (arrowheads) in the medial aspect of the proximal tibial metaphysis with cortical erosion (arrow).

Haemophilic

pseudotumour. Axial T1-WI fat-saturated image show a heterogenous periosteal lesion in the tibial metaphysis with areas with high signal (*), translating the presence of metheamoglobin (subacute haemorrhage). The lesion extends to the soft tissues.

Haemophilic

pseudotumour. Coronal T1-WI image shows a heterogeneous lesion in the tibial metaphysis with areas with high signal (*), translating the presence of metheamoglobin (subacute haemorrhage). There is elevation of periosteum with areas of focal erosion (arrow).

Haemophilic

pseudotumour. Sagittal T2-WI image with fat saturation show linear hypointense areas (white arrow) which translate haemosiderin deposits (bleeding in chronic phase). Increased signal intensity of bone marrow (black arrow) adjacent to the lesion (oedema).

Haemophilic

pseudotumour. Axial T1-WI fat saturation image after gadolinium intravenous injection show peripheral contrast uptake of the lesion (arrow).