Ossifying fibromyxoid tumors

Imaging of
incidentally discovered ossifying fibromyxoid tumour of retroperitonuem with histopathological correlation: a rare case report. Contrast-enhanced arterial phase axial CT image of the abdomen shows a well-defined moderately enhancing lesion in the left para-aortic region seen closely abutting the left psoas muscle.
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Imaging of
incidentally discovered ossifying fibromyxoid tumour of retroperitonuem with histopathological correlation: a rare case report. Contrast-enhanced Delayed-phase axial CT image of abdomen shows persistent enhancing areas within the lesion. A focus of calcification is also evident.
www.eurorad.org • CC by-nc-sa-4.0
Malignant
ossifying fibromyxoid tumor of the tongue: case report and review of the literature. Findings of the mass in the tongue. A: Progressive swelling mass was founded at the tongue. B: Ultrasonographic findings showing a soft tissue mass. C: The cut section surface of the tumor was gray- white, solid, and firm in consistency.
head-face-med.biomedcentral.com • CC-by-2.0
Ossifying
Fibromyxoid tumor of soft parts in head and neck: case report and literature review. Extraoral photograph shows a mass in the patient’s right submandibular region (a). Coronal head CT scan shows a mixed lesion (outlined by the dotted line) near the right submandibular gland (b)
diagnosticpathology.biomedcentral.com • CC-by-4.0
Response to
isolated limb perfusion and chemotherapy with epirubicin plus ifosfamide in a metastatic malignant ossifying fibromyxoid tumor. Axial contrast enhanced T1-weighted MRI. Pathologic tissue in the hypothenar eminence of the right hand, involving the flexor tendons and the spaces between 3rd, 4th and 5th metacarpal bones with intense and homogeneous contrast enhancement (a). Progressive size and contrast enhancement reduction after ILP (b), and chemotherapy (c)
clinicalsarcomaresearch.biomedcentral.com • CC-by-4.0
Radiopaedia • CC-by-nc-sa 3.0 • de

Ossifying fibromyxoid tumor (OFMT) is a soft tissue tumor of uncertain lineage.

Epidemiology

It typically manifests in adults. There may be a slight increased male predilection.

Clinical presentation

The clinical presentation can vary depending on location but usually tends to manifest as a slowly growing painless mass.

Pathology

Its exact etiology is not very clear but a schwannian or chondroid origin has sometimes been favored. It comprises of small round cells dispersed in a myxoid matrix and can contain bone, osteoid, and collagen elements.

Location

It is reported to most often arise in the subcutaneous extremities.

Other reported locations include

Treatment and prognosis

It is generally considered benign although recurrence following the resection can be common. Complete local resection is considered the best treatment in many cases.

See also

  • soft tissue tumors (classification) - WHO 2002
Siehe auch:
Assoziationen und Differentialdiagnosen zu ossifizierender fibromyxoider Tumor:
Myxom
 
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