Rapidly progressive interstitial lung disease (RP-ILD)
Rapidly progressive interstitial lung disease (RP-ILD) is a temporal descriptive term for forms interstitial lung disease which can progress rapidly through time (a quantitative census on the temporal time frame however has not been published at the the time of the study (i.e. there is some subjectivity). There is also no clear morphological descriptor for this pattern.
Situations in which this has been described:
- anti-MDA5 antibody-positive amyopathic dermatomyositis associated interstitial lung disease
- interstitial lung disease associated with systemic sclerosis (SSc-ILD)
- acute interstitial pneumonitis (AIP)
- forms of acute respiratory distress syndrome (ARDS): debatable as to if this should be in this group as often it is the acute pneumonic process that progresses rather than the fibrotic component
See also
