Askin tumor

Teenager with
fever and left pleuritic chest pain. CXR PA and lateral (above) show a round mass on the lateral and middle aspect of the dome of the left hemidiaphragm. Axial CT with contrast of the chest (below) shows the soft tissue mass to be arising from a rib which has extensive and aggressive periosteal reaction.The diagnosis was Ewing sarcoma of the rib (Askin tumor).
pediatricimaging.org • CC-by-nc-sa 4.0
School ager
with right scapular and right chest pain. CXR AP and lateral (above) show a large right sided chest mass whose obtuse angles with the chest wall suggest it is extrapleural in origin. Axial CT without contrast of the chest (below) shows the mass to be arising from a rib and to be causing periosteal reaction.The diagnosis was Ewing sarcoma of the rib (Askin tumor).
pediatricimaging.org • CC-by-nc-sa 4.0
Ewing sarcoma
family of tumors • Ewing sarcoma of the chest wall - Ganzer Fall bei Radiopaedia
Saber M, Ewing sarcoma of the chest wall. Case study, Radiopaedia.org (Accessed on 19 Nov 2022) https://doi.org/10.53347/rID-88321 • CC by-nc-sa 3.0 (modified)
Radiopaedia • CC-by-nc-sa 3.0 • de

The original description of the Askin tumor (by Askin and Rosai in 1979 ), and many studies following it have led to a great deal of confusion. Until recently it has been considered a separate entity or as a type of peripheral primitive neuroectodermal tumor, usually of the chest wall.

However, recent genetic research has led to the conclusion that it is essentially the same as Ewing sarcoma, and now is part of the collective term Ewing sarcoma family of tumors, sharing similar demographics, imaging findings and prognosis . Please see Ewing sarcoma of the chest wall for more detail.

While histologically the tumors are similar to an Ewing sarcoma, their typical location and growth pattern make the tumor a distinct radiographic entity.