Jaffe-Campanacci syndrome
Jaffe-Campanacci-Syndrome,
boy 7 Y, tibial bowing and cortical/subcortial mixed sclerosis
Osteofibrous
dysplasia-like adamantinoma treated via intercalary segmental resection with partial cortex preservation using pedicled vascularized fibula graft: a case report. The X-ray, CT image, and MR images of the tumor. a Anteroposterior radiograph. b Lateral radiograph. c Axial CT image. d T1-weighted magnetic resonance sagittal image. e T2-weighted magnetic resonance sagittal image
Osteofibrous
dysplasia-like adamantinoma treated via intercalary segmental resection with partial cortex preservation using pedicled vascularized fibula graft: a case report. The mass was a heterogeneously hypointense and isointense on a T1-weighted magnetic resonance image and b heterogeneously hyperintense on short TI inversion recovery magnetic resonance image. No pathological fracture was confirmed
Osteofibrous
dysplasia • Osteofibrous dysplasia of the tibia - Ganzer Fall bei Radiopaedia
Osteofibrous
dysplasia • Osteofibrous dysplasia of the tibia - Ganzer Fall bei Radiopaedia
Osteofibrous
dysplasia • Osteofibrous dysplasia - tibia - Ganzer Fall bei Radiopaedia
Osteofibrous
dysplasia • Osteofibrous dysplasia - Ganzer Fall bei Radiopaedia
Osteofibrous
dysplasia • Osteofibrous dysplasia - Ganzer Fall bei Radiopaedia
Teenager with
neurofibromatosis type I and knee pain. AP and lateral radiographs of the knee show multiple lucent lesions with thin sclerotic margins in the metaphysis of the femur, tibia and fibula.The diagnosis was multiple non ossifying fibromas in Jaffe Campanacci Syndrome in a patient with neurofibromatosis type I.
nicht verwechseln mit: Fibröse DysplasieJaffe-Campanacci syndrome is characterized by:
- multiple non-ossifying fibromas of the long bones and jaw
- café au lait spots
- intellectual disability
- kyphoscoliosis
- hypogonadism or cryptorchidism
- ocular malformations
- cardiovascular malformations
- giant cell granuloma of the jaw
History and etymology
It is named after Mario Campanacci, Italian physician (1932-1999), and Henry Lewis Jaffe, American pathologist (1896-1979) .
Differential diagnosis
Consider:
Siehe auch:
- Osteoid-Osteom
- nicht ossifizierendes Fibrom
- Fibröse Dysplasie
- Kryptorchismus
- Ossifizierendes Fibrom
- Adamantinom der langen Röhrenknochen
- Admantinom mit dem Bild einer osteofibrösen Dysplasie
und weiter:

Assoziationen und Differentialdiagnosen zu Jaffé-Campanacci-Syndrom: