Ossifying renal tumor of infancy

Ossifying renal tumor of infancy (ORTI) is a rare renal tumor.

Epidemiology

  • extremely rare, <<1% of pediatric renal neoplasms (17 cases reported)
  • 6 days - 3 months
  • male predominant

Pathology

Histology reveals spindle cells and osteoblastic cells in a calcified osteoid matrix. It is thought to originate from intralobar nephrogenic rests.

Radiographic features

Abdominal radiography
Ultrasound
  • calcification is hyperechoic
  • there may be intra-tumoral flow on color Doppler ultrasound
CT

ORTI may resemble a staghorn calculus since it originates from the renal papilla, but it enhances postcontrast.

Treatment and prognosis

Cases of ORTI so far have been benign, with no recurrence after resection.

Differential diagnosis

Siehe auch: