Pulmonary hypertension (2003 classification)
Pulmonary hypertension (2003 classification)
There are numerous causes of pulmonary hypertension, and thus not surprisingly there have been many classification systems.
In 2003, the 3 World Symposium on PAH met in Venice and produced an updated classification system (this has been further revised in the Dana Point classification of pulmonary hypertension).
- idiopathic (IPAH)
- familial (FPAH)
- associated with (APAH):
- connective tissue disease
- congenital systemic to pulmonary shunts
- portal hypertension
- HIV infection - HIV-associated pulmonary arterial hypertension
- drugs and toxins
- other (thyroid disorders, glycogen storage disease, Gaucher disease, hereditary hemorrhagic telangiectasia, hemoglobinopathies, myeloproliferative disorders, splenectomy)
- associated with significant venous or capillary involvement
- persistent pulmonary hypertension of the newborn (PPHN)
- left-sided atrial or ventricular heart disease
- left-sided valvular heart disease
- chronic obstructive pulmonary disease (COPD)
- interstitial lung disease
- sleep disordered breathing
- alveolar hypoventilation disorders
- chronic exposure to high altitude
- developmental abnormalities
- thromboembolic obstruction of proximal pulmonary arteries
- thromboembolic obstruction of distal pulmonary arteries
- non-thrombotic pulmonary embolism (tumor, parasites, foreign material)
- sarcoidosis
- Langerhans cell histiocytosis (LCH / histiocytosis X)
- lymphangioleiomyomatosis (LAM)
- compression of pulmonary vessels
- lymphadenopathy
- tumor
- fibrosing mediastinitis
Siehe auch:
- Sarkoidose
- Lymphangioleiomyomatose
- Histiozytose X
- Chronisch obstruktive Lungenerkrankung
- Interstitielle Lungenerkrankung
- pulmonale Hypertonie
- pulmonale venookklusive Erkrankung
- pulmonale kapilläre Hämangiomatose
- idiopathic pulmonary arterial hypertension (IPAH)
- fibrosierende Mediastinitis
und weiter:
Assoziationen und Differentialdiagnosen zu Pulmonary hypertension (2003 classification):
