pancreatic dorsal agenesis

Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Unenhanced images (a, detail b) showed truncated pancreas (arrowheads) at transition between neck and body; pancreatic head containing tiny calcifications, a demarcated 2-cm hypodense ovoid lesion (arrow) at the uncinate process.
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Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Unenhanced images (a, detail b) showed truncated pancreas (arrowheads) at transition between neck and body; pancreatic head containing tiny calcifications.
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Corresponding portal venous phase enhanced images (c, detail d) confirmed rounded, truncated pancreas (arrowhead) at transition between neck and body; tiny pancreatic calcifications; a non-enhancing demarcated 2-cm ovoid lesion (arrow) at the uncinate process.
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Corresponding portal venous phase enhanced images (c, detail d) confirmed rounded, truncated pancreas (arrowhead) at transition between neck and body; tiny pancreatic calcifications; a non-enhancing demarcated 2-cm ovoid lesion (arrow) at the uncinate process.
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Coronal contrast-enhanced image confirmed pancreatic head with tiny pancreatic calcifications; a ductal structure (thin arrow), a non-enhancing demarcated 2-cm ovoid lesion (arrow) at the uncinate process. Note absent pancreatic body and tail, dilated splenic vein (*).
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Cranial axial image confirmed absent pancreatic body and tail; patent dilated splenic vein (*).
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Axial T2-weighted image confirmed absent pancreatic body and tail in their normal anatomic location adjacent to the splenic vein (*).
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Axial (b), coronal (c) T2- and axial T1-weighted (d) images confirmed inhomogeneous pancreatic head with two cystic lesions (arrows), the largest measuring 2 cm in the uncinate process.
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Coronal (c) T2- and axial T1-weighted (d) images confirmed inhomogeneous pancreatic head with two cystic lesions (arrows), the largest measuring 2 cm in the uncinate process. Note absent pancreatic body and tail, splenic vein (*).
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. Axial T1-weighted image confirmed truncated pancreas (arrowhead) at transition between neck and body, absent pancreatic body and tail.
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. MRCP (e, f) confirmed two cystic pancreatic lesions (arrows), the largest in the uncinate process, and visualized a normal-calibre pancreatic duct (thin arrows) draining into the Vaterian ampulla. Normal biliary tract.
www.eurorad.org • CC by-nc-sa-4.0
Partial
agenesis of the pancreas with superimposed chronic pancreatitis. MRCP (e, f) confirmed two cystic pancreatic lesions (arrows), the largest in the uncinate process, and visualized a normal-calibre pancreatic duct (thin arrows) draining into the Vaterian ampulla. Normal biliary tract.
www.eurorad.org • CC by-nc-sa-4.0
Radiopaedia • CC-by-nc-sa 3.0 • de

Agenesis of the dorsal pancreas is an extremely rare congenital pancreatic anomaly.

While complete agenesis of the dorsal pancreas is extremely rare, partial agenesis of the dorsal pancreas is thought to be more common than ventral pancreatic agenesis .

Clinical presentation

While many patients with this anomaly are asymptomatic, some patients may present with abdominal pain .

Pathology

It results from an embryological failure of the dorsal pancreatic bud to form the body and tail of the pancreas.

Partial dorsal pancreatic agenesis may be appreciated as a short, rounded pancreatic head adjacent to the duodenum with absence of the pancreatic neck, body, and tail. With complete agenesis of the dorsal pancreas, the neck, body, and tail of the pancreas, the duct of Santorini, and the minor duodenal papilla are all absent. With partial agenesis of the dorsal pancreas, the size of the body of the pancreas varies, there is a remnant of the duct of Santorini, and the minor duodenal papilla is present.

Associations

Radiographic features

CT
  • the pancreatic body and tail are hypoplastic or absent to varying degrees with preservation of the pancreatic head
  • some reports suggest an enlarged pancreatic head (but only in a proportion of cases with this anomaly)

See also

Siehe auch:
und weiter:
Assoziationen und Differentialdiagnosen zu Agenesie der dorsalen Pankreasanlage:
Pankreatitis
 
Wikipedia • CC BY-SA 3.0
solider
pseudopapillärer Tumor des Pankreas
insightsimaging.springeropen.com • CC-by-4.0
Normvarianten
der Pankreasgänge
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polysplenia
 
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