Pulmonalvenenatresie
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Unilateral
pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report. a Expectorant consisted of fresh bright blood mixed with small clots and mucus. b Chest radiograph showing ambiguous situs (abnormal liver and stomach position), mesocardia and a mass over the right para-cardiac region. c Bronchoscopic image of right main bronchus showing mucosal hyperaemia, oedema and variceal engorgement of submucosal blood vessels
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Unilateral
pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report. Volume-rendered reconstructed image of cardiac CT showing absence of right pulmonary veins with smooth appearance of adjacent posterior left atrial wall (white arrows). LA = left atrium, RPA = right pulmonary artery, LPA = left pulmonary artery, LPV = left pulmonary veins
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Unilateral
pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report. Multiplanar reconstructed cardiac CT images. a Significant size discrepancy between right and left pulmonary arteries. b Right lung parenchymal changes with diffuse interlobular septal thickening and mosaic attenuation. c Systemic-to-pulmonary collateral artery (white arrows) from the coeliac artery supplying the right lung. The hepatic segment of inferior vena cava is interrupted. d Both atrial appendages are long and narrow; characteristic of left atrial isomerism. e Both upper lobar bronchi course below the respective pulmonary arteries (hyparterial bronchi) which is typical of left bronchial isomerism. f Lobulated spleen which is a variant of polysplenia. Also shown is part of the dilated azygous vein. RPA = right pulmonary artery, LPA = left pulmonary artery, CHD = congenital diaphragmatic hernia, IVC = inferior vena cava, LAA = left atrial appendage, Azyg = azygous vein, S = spleen
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Unilateral
pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report. A Postero Anterior chest x-ray (PA CXR). Left hemithorax appears smaller and diffuse reticulation with smaller hilum. Right hemithorax is normal. B Contrast enhanced chest Computed tomography showing left lung diffuse interlobular septal thickening and ground glass opacity with a normal right lung. Note the significantly smaller left pulmonary artery (smaller arrow) as compared to the right (bigger arrow)
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Unilateral
pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report. A Axial view Computed tomography angiography showing Left Atrium (∆), right upper (−) and right lower ( +) pulmonary veins. Left boarder of left atrium is smooth (arrows). Vascular anastomosis appears as a left hilar ill-defined mass (x). B Left posterior corona image of Computed tomography angiography with smooth Left Atrium (curved arrow) on the left and branching pulmonary veins on the right ( +). Left hilar vascular anastomosis (x) also seen
Pulmonary vein atresia represents to a spectrum of disorders where the pulmonary veins fail to form to varying degrees.
It can be broadly divided into:
- unilateral pulmonary vein atresia
- bilateral pulmonary vein atresia - common pulmonary vein atresia
See also
- anomalous pulmonary venous drainage
- cor triatriatum
Siehe auch:
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