benignes fibröses Histiozytom des Knochens
A rare case
of benign fibrous histiocytoma of the iliac bone. X-ray image of the pelvis shows an expansile lytic lesion with cortical disruption and few bony septations in left iliac bone with no evidence of periosteal reaction and marginal sclerosis. No evidence of matrix calcification.
A rare case
of benign fibrous histiocytoma of the iliac bone. PLAIN CT of pelvis in axial and coronal plane shows a large homogenous soft tissue density lesion in left iliac bone with cortical disruption.
A rare case
of benign fibrous histiocytoma of the iliac bone. Fig. 3A-T1W Axial image. MRI images of pelvis show a well-defined T1W and T2W hypointense lesion (3a, b) in left iliac bone with no diffusion restriction (3c, d). Post-contrast images (3e, f) show peripheral enhancement of the lesion with central non-enhancing area.
A rare case
of benign fibrous histiocytoma of the iliac bone. Fig 3B- T2W Axial image. MRI images of pelvis show a well-defined T1W and T2W hypointense lesion (3a, b) in left iliac bone with no diffusion restriction (3c, d). Post-contrast images (3e, f) show peripheral enhancement of the lesion with central non-enhancing area.
A rare case
of benign fibrous histiocytoma of the iliac bone. Fig 3C- DWI. MRI images of pelvis show a well-defined T1W and T2W hypointense lesion (3a, b) in left iliac bone with no diffusion restriction (3c, d). Post-contrast images (3e, f) show peripheral enhancement of the lesion with central non-enhancing area.
A rare case
of benign fibrous histiocytoma of the iliac bone. Fig 3D- ADC. MRI images of pelvis show a well-defined T1W and T2W hypointense lesion (3a, b) in left iliac bone with no diffusion restriction (3c, d). Post-contrast images (3e, f) show peripheral enhancement of the lesion with central non-enhancing area.
A rare case
of benign fibrous histiocytoma of the iliac bone. Fig 3E- T1 FS post-contrast axial image. MRI images of pelvis show a well-defined T1W and T2W hypointense lesion (3a, b) in left iliac bone with no diffusion restriction (3c, d). Post-contrast images (3e, f) show peripheral enhancement of the lesion with central non-enhancing area.
A rare case
of benign fibrous histiocytoma of the iliac bone. Fig 3F- T1 FS post-contrast sagittal image. MRI images of pelvis show a well-defined T1W and T2W hypointense lesion (3a, b) in left iliac bone with no diffusion restriction (3c, d). Post-contrast images (3e, f) show peripheral enhancement of the lesion with central non-enhancing area.
Benign
fibrous histiocytoma of bone • Benign fibrous histiocytoma - Ganzer Fall bei Radiopaedia
Benign
fibrous histiocytoma of bone • Benign fibrous histiocytoma - Ganzer Fall bei Radiopaedia
Benign
fibrous histiocytoma of bone • Benign fibrous histiocytoma - Ganzer Fall bei Radiopaedia
Benign
fibrous histiocytoma of bone • Deep benign fibrous histiocytoma - Ganzer Fall bei Radiopaedia
Benign fibrous histiocytoma is closely related to fibroxanthoma of bone, is a rare lesion usually occurring in the skin where it is known as dermatofibroma.
Clinical presentation
Typically presents with pain, and most often in the third decade.
Pathology
Only a few case reports have been published but locations these have occurred include:
- ribs
- pelvis: including the sacrum and ilium
- tubular bones: epiphysis or diaphysis
- commonly seen around the knee
Radiographic features
Plain film and CT
- lytic, loculated, with prominent sclerotic border
- narrow zone of transition
- no matrix mineralization
- cortical expansion and soft tissue invasion are rarely seen
MRI
- T1
- central low signal intensity
- peripheral enhancement
- T2
- heterogeneous high signal intensity
- low signal in surrounding sclerotic bone
Bone scan
- may be positive
Treatment and prognosis
Surgical resection. Local recurrence is ~15% (range 5-25%).
Differential diagnoses
- non-ossifying fibroma
- younger patients
- usually no pain
- more prominent marginal sclerosis
- no uptake on bone scan
Siehe auch:
Assoziationen und Differentialdiagnosen zu benignes fibröses Histiozytom des Knochens:
