Pulmonary vein atresia

Unilateral

pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report. a Expectorant consisted of fresh bright blood mixed with small clots and mucus. b Chest radiograph showing ambiguous situs (abnormal liver and stomach position), mesocardia and a mass over the right para-cardiac region. c Bronchoscopic image of right main bronchus showing mucosal hyperaemia, oedema and variceal engorgement of submucosal blood vessels

Unilateral

pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report. Volume-rendered reconstructed image of cardiac CT showing absence of right pulmonary veins with smooth appearance of adjacent posterior left atrial wall (white arrows). LA = left atrium, RPA = right pulmonary artery, LPA = left pulmonary artery, LPV = left pulmonary veins

Unilateral

pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report. Multiplanar reconstructed cardiac CT images. a Significant size discrepancy between right and left pulmonary arteries. b Right lung parenchymal changes with diffuse interlobular septal thickening and mosaic attenuation. c Systemic-to-pulmonary collateral artery (white arrows) from the coeliac artery supplying the right lung. The hepatic segment of inferior vena cava is interrupted. d Both atrial appendages are long and narrow; characteristic of left atrial isomerism. e Both upper lobar bronchi course below the respective pulmonary arteries (hyparterial bronchi) which is typical of left bronchial isomerism. f Lobulated spleen which is a variant of polysplenia. Also shown is part of the dilated azygous vein. RPA = right pulmonary artery, LPA = left pulmonary artery, CHD = congenital diaphragmatic hernia, IVC = inferior vena cava, LAA = left atrial appendage, Azyg = azygous vein, S = spleen

Unilateral

pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report. A Postero Anterior chest x-ray (PA CXR). Left hemithorax appears smaller and diffuse reticulation with smaller hilum. Right hemithorax is normal. B Contrast enhanced chest Computed tomography showing left lung diffuse interlobular septal thickening and ground glass opacity with a normal right lung. Note the significantly smaller left pulmonary artery (smaller arrow) as compared to the right (bigger arrow)

Unilateral

pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report. A Axial view Computed tomography angiography showing Left Atrium (∆), right upper (−) and right lower ( +) pulmonary veins. Left boarder of left atrium is smooth (arrows). Vascular anastomosis appears as a left hilar ill-defined mass (x). B Left posterior corona image of Computed tomography angiography with smooth Left Atrium (curved arrow) on the left and branching pulmonary veins on the right ( +). Left hilar vascular anastomosis (x) also seen