Primary pulmonary chondrosarcoma
Primary pulmonary chondrosarcoma is an extremely rare form of chondrosarcoma, in terms of location. The majority of intrathoracic chondrosarcomas occur in relation to the chest wall.
Epidemiology
While the exact incidence is unknown, only a handful of cases have been reported in the literature.
Pathology
Markers
Tumors can be positive for the S100 protein .
Radiographic features
They can be variable in size with some reports stating 2-11 cm at time of presentation.
Treatment and prognosis
As with other chrondrosarcoma, it usually grows slowly, tends to metastasize late, and often responds well to excision when localized.
See also
