Kolibri-Zeichen Mittelhirn
This patient
presented with progressive dementia, ataxia and incontinence. A clinical diagnosis of normal pressure hydrocephalus was entertained. Imaging did not support this, however, and on formal testing abnormal nystagmus and eye movements were detected. A sagittal T1-weighted image shows atrophy of the midbrain, with preservation of the volume of the pons. This appearance has been called the "penguin sign". There is also atrophy of the tectum, particularly the superior colliculi. These findings suggest the diagnosis of en:progressive supranuclear palsy.
Imaging
biomarkers in Parkinson’s disease and Parkinsonian syndromes: current and emerging concepts. MRI of a patient with a clinical diagnosis of Progressive Supranuclear Palsy. The image on the left is a sagittal T1 sequence showing the ‘Hummingbird’ sign (box), while the axial T1 sequence on the right shows the ‘Morning Glory’ sign (arrows) both features seen in Progressive Supranuclear Palsy
Hummingbird
sign (midbrain) • Hummingbird (photo) - Ganzer Fall bei Radiopaedia
Hummingbird
sign (midbrain) • Hummingbird appearance in midbrain atrophy - Ganzer Fall bei Radiopaedia
Progressive
supranuclear palsy • Progressive supranuclear palsy - with hummingbird or penguin sign - Ganzer Fall bei Radiopaedia
The hummingbird sign, also known as the penguin sign, refers to the appearance of the brainstem in patients with progressive supranuclear palsy (PSP).
The atrophy of the midbrain results in a profile of the brainstem (in the sagittal plane) in which the preserved pons forms the body of the bird, and the atrophic midbrain the head, with beak extending anteriorly towards the optic chiasm. Midbrain atrophy is best confirmed with reduction in the midbrain to pons ratio.
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Assoziationen und Differentialdiagnosen zu Kolibri-Zeichen Mittelhirn:
