Cenani Lenz syndactyly

Cenani-Lenz syndactyly (CLS) is a very syndrome primarily characterized by:

  • syndactyly/oligodactly: syndactyly is often complete and gives a spoon hand type appearance
  • radio-ulnar synostoses

Pathology

Genetics

It carries an autosomal recessive inheritance.

Etymology

It was first described by Asim Cenani, a Turkish medical geneticist and Widukind Lenz, a German medical geneticist in 1967 .

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