proximal radio-ulnar synostosis
Proximal radio-ulnar synostosis is an upper limb skeletal malformation characterized by bony fusion at the proximal aspect of the radius and ulna. Of the radio-ulnar synostoses, the proximal third is considered the most common site.
Pathology
It is often congenital but can rarely result following trauma. A developmental relationship between posterior dislocation of the radial head and proximal radioulnar fusion has been suggested by some authors.
Associations
Several associated conditions have described including :
- Poland syndrome
- Cornelia de Lange syndrome
- chromosomal anomalies (including tetrasomy X)
- Cenani Lenz syndactyly
Siehe auch:
Assoziationen und Differentialdiagnosen zu proximal radioulnar synostosis:
