cochlear aplasia

Cochlear aplasia, or complete absence of the cochlea is a rare anomaly which accounts for only 3% of cochlear malformations.

Radiographic features

Differential diagnosis

  • labyrinthitis ossificans
    • normal-sized bone is seen anterior to the IAC
    • the bulge of the cochlear promontory produced by the basal turn of the cochlea is present
  • common cavity deformity
  • cystic cochleovestibular anomaly
  • labyrinthine aplasia

See also

Siehe auch: