Cochlear incomplete partition
Pre- and
post-operative imaging of cochlear implants: a pictorial review. A 1-year-old male patient, with sensorineural deafness from birth. HRCT axial image (left) and coronal image (right) show incomplete partition type I, with empty cystic cochlea (C) and a large dilated vestibulum (V). Stapes is malformed and fused with the incus (arrow)
Pre- and
post-operative imaging of cochlear implants: a pictorial review. A 12-year-old male patient, with bilateral severe SNLH from birth. HRCT axial images show incomplete partition type II with the cystic apex of the cochlea (arrow) and enlarged vestibular aqueduct (asterisk). Vestibulum is minimally enlarged (dashed arrow), and semicircular canals appear normal
Pre- and
post-operative imaging of cochlear implants: a pictorial review. A 1-year-old male patient, with bilateral severe SNLH from birth. HRCT axial image shows incomplete partition type III with empty cochlea with preserved interscalar septa (arrowhead). Modiolus and bony separation of the cochlea and internal auditory canal are absent (arrow). The cochlea is placed directly at the lateral end of the internal auditory canal (asterisk)
Pre- and
post-operative imaging of cochlear implants: a pictorial review. A 1-year-old male patient, with bilateral severe SNHL from birth. HRCT axial image (left image) shows incomplete partition type I with cystic cochlea (C) and vestibulum (V). The horizontal segment of the facial nerve (arrow) is lateralized. HRCT coronal image (right image) shows an interrupted line corresponding to the most lateral aspect of the vertical segment of the facial nerve (open arrow) lateral to the continuous line corresponding to the most lateral bony aspect of the lateral semicircular canal. The normal location of the vertical segment is medial to the lateral semicircular canal
Cochlear incomplete partition is a group of cochlear malformations associated with variable other inner ear architecture defects. These malformations have in common that the cochlea is clearly separated from the vestibule and the external contour of the cochlear is nearly normal in size, but there are defects involving the modiolus and interscalar septa .
According to the CT-based classification that Sennaroglu proposed in 2002 and subsequently revised , there are three types of incomplete partition:
- cochlear incomplete partition type I (IP-I)
- also known as cystic cochleovestibular malformation
- cochlear incomplete partition type II (IP-II)
- when associated with enlarged vestibule aqueduct and mildly dilated vestibule, the triad is known as Mondini malformation
- cochlear incomplete partition type III (IP-III)
- observed in X-linked deafness
See also
Siehe auch:
