Currarino-Silverman syndrome

Currarino-Silverman syndrome, also known as pectus carinatum type 2 deformity, is a rare disorder.

Clinical presentation

Patients present with a high carinate chest deformity due to a premature fusion of the manubriosternal joint and sternal ossification centers. Congenital heart diseases have been described in more than 50% of the patients .

The majority of cases are symmetric, but asymmetric and even mixed deformities (e.g. ipsilateral carinatum and contralateral excavatum) may occur. Other associated musculoskeletal abnormalities may be present, such as scoliosis and, in rare cases, Poland syndrome.

Treatment and prognosis

Surgical correction can be done by bilateral resection of the third through seventh costal cartilages and osteotomy, usually with a satisfactory result.

History and etymology

Described by the American pediatric radiologists Guido Currarino and Frederic N Silverman in 1958 .