deafness
Extremely
discrepant mutation spectrum of SLC26A4 between Chinese patients with isolated Mondini deformity and enlarged vestibular aqueduct. Typical CT scan images of MD, EVA with MD, EVA, and other inner ear malformations. a. MD; b. EVA with MD; c. EVA; d. common cavity (a cystic cavity representing the cochlea and vestibule without showing any differentiation into cochlea and vestibule); e. narrow internal auditory canal; f. internal auditory canal enlarged; g. inner ear ossification; h. cochlear, vestibular, and semicircular canal hypoplasia.
Deafness (also known as hearing loss or impairment) is the partial or complete loss of the sense of hearing.
It may be subdivided etiologically into
- conductive: impairment of the passage of sound waves from the auricle to the inner ear
- sensorineural: impairment localizes to the inner ear, internal acoustic canal, cerebellopontine angle, or vestibulocochlear nerve
- central: impairment is central to the vestibulocochlear nerve i.e. in the brain
- sometimes these causes are counted as a subtype of sensorineural deafness
- functional: no organic cause identified
Siehe auch:
- Otosklerose
- Schwerhörigkeit
- Keratitis-Ichthyosis-Taubheitssyndrom
- Innenohrschwerhörigkeit
- Albinismus-Taubheit-Syndrom
- Konigsmark-Hollander-Berlin-Syndrom
- Bart-Pumphrey-Syndrom
und weiter:
Assoziationen und Differentialdiagnosen zu Gehörlosigkeit: