Fibröse Dysplasie des proximalen Femurs

Fibrous

dysplasia for radiologists: beyond ground glass bone matrix. The radiographic appearance of fibrous dysplasia (FD) and the rind sign. a–e Frontal radiographs demonstrate classic FD lesions in appendicular skeleton. A classic lucent lesion surrounded by a layer of sclerotic reactive bone (so-called the rind sign). The rind sign is most commonly seen in the proximal femur (red arrow)

Fibrous

dysplasia for radiologists: beyond ground glass bone matrix. MRI in fibrous dysplasia (FD). a, b MRI typically shows sharply demarcated lesions with intermediate to low signal intensity on T1-weighted images (WI) and intermediate to high on T2-WI (red arrow). c Some FD lesions may also contain small cystic areas, which make the T2 signal bright (green arrow). d FD lesions usually show some degree of enhancement after contrast administration (blue arrow)

Fibrous

dysplasia for radiologists: beyond ground glass bone matrix. “Evolution” of the fibrous dysplasia (FD) lesions. a Radiograph of a 3-year-old demonstrates a typical heterogeneous-appearing FD lesion in the femur. b Radiograph from an 11-year-old demonstrates homogeneous and radiolucent FD lesion. c Image from a 54-year-old patient shows sclerotic FD lesions

McCune-Albright

syndrome. CT for detecting subtle fractures. A) This radiograph was from a 9-year-old boy who complained of new-onset, focal pain in the groin. No discernable fracture is apparent. B) Reformatted CT images of the lesion revealed a fracture in the medial proximal femur (arrows).

Surgical

treatment for fibrous dysplasia of femoral neck with mild but prolonged symptoms: a case series. Patient 4. A 32-year-old female presented with repeated bilateral hip pain for 20 years. An A-P X-ray at the time of initial referral indicated fibrous dysplasia of her right femoral neck and “parrot’s beak” sign (arrows)

Surgical

treatment for fibrous dysplasia of femoral neck with mild but prolonged symptoms: a case series. Patient 4. X-ray at the time of surgery after fixation with a compression hip screw (a). Nine years after surgery, a grafted fibular strut was well preserved (b, arrows)

Surgical

treatment for fibrous dysplasia of femoral neck with mild but prolonged symptoms: a case series. Patient 1. A 22-year-old female presented with repeated or persistent right hip pain since for ten years. An A-P X-ray at the initial presentation indicated fatigue fracture with “parrot’s beak” sign (white arrows) (a). X-rays at three years (b) and ten years (c) after surgery revealed cure of the fatigue fracture and preservation of the grafted autogenous fibular strut (black arrows)