idiopathic, pauci-immune pulmonary capillaritis (IPIPC)
Idiopathic pauci immune pulmonary capillaritis (IPIPC) is considered a rare type of pulmonary vasculitis. Some authors consider this due be an organ specific subset of microscopic polyangiitis . It can result in diffuse alveolar hemorrhage.
Pathology
It is an isolated small vessel vasculitis that by definition is isolated to the lungs and, hence, presents with diffuse alveolar hemorrhage as its primary clinical manifestation. Some (but not all) cases can have pANCA positivity .
History and etymology
It was thought have been first described by Nierman et.al in 1995and then fully charaterised by Jennings et.al in 1997 .
See also
Siehe auch:
und weiter:
Assoziationen und Differentialdiagnosen zu idiopathic, pauci-immune pulmonary capillaritis (IPIPC):
