lenticonus
Lenticonus is a rare congenital abnormality characterized by conical bulging of the posterior or anterior lens surface. If the bulging is global rather than conical, the condition is referred to as lentiglobus .
Clinical presentation
It produces a decrease in visual acuity and irregular refraction that cannot be corrected by either spectacle or contact lenses.
Pathology
Subtypes
- anterior lenticonus
- often bilateral
- >90% of cases are associated with Alport syndrome
- posterior lenticonus
- more common, unilateral and axial in location