Pai syndrome (midline cleft of the upper lip - facial skin polyps - central nervous system lipomas)

Fibrolipoma

of the nasal septum; report of the first case. (A) Computed tomography showing a 25x12 mm low density mass in the nasal septum. (B) T2 weight magnetic resonance (MR) imaging presenting a high signal intensity 22x12 mm mass. (C) MRI showing a lipoma, 18 mm thick and 51 mm in length at the level of falx cerebri that pushed the corpus callosum and reaching the cingulate gyrus anteroposteriorly.

Lipoma of

Columella with septal extension in Pai syndrome: report of a rare case. CECT Coronal view -Lipoma in the genu of corpus callosum and nasal tip with obliteration of right nasal cavity