Pulmonary vein stenosis

Pulmonary vein stenosis refers to a spectrum of conditions characterized by narrowing of the pulmonary veins. It can be congenital or acquired.

• primary pulmonary vein stenosis - occurs in children
• secondary pulmonary vein stenosis - occurs in adults and usually associated with some identifiable underlying causative process
  • involvement of the pulmonary veins by an extrinsic process
    • neoplasm growth
    • sarcoidosis
    • fibrosing mediastinitis
  • iatrogenic procedures - radiofrequency ablation for atrial fibrillation (1-3% of cases ).
  • post-surgical e.g. post-repair of anomalous pulmonary venous return

Complications

Recognized complications include

• pulmonary hypertension - pulmonary hypertensive crisis
• recurrent intercurrent pulmonary infection
• hemoptysis

See also

• pulmonary vein
• pulmonary vein thrombosis
• pulmonary vein atresia

Siehe auch:

• Sarkoidose
• fibrosierende Mediastinitis
• Pulmonalvenenthrombose