embryonales Rhabdomyosarkom
Imaging of
parotid anomalies in infants and children. Embryonic rhabdomyosarcoma. Heterogeneous structure and vascularization on B-mode sonography and color Doppler (a and b), large at the time of diagnosis on frontal T2-weighted image (c)
Embryonal
rhabdomyosarcoma • Embryonal rhabdomyosarcoma - Ganzer Fall bei Radiopaedia
Embryonal
rhabdomyosarcoma • Embryonal rhabdomyosarcoma of the soft palate - Ganzer Fall bei Radiopaedia
The embryonal subtype of rhabdomyosarcoma is the most common variety of rhabdomyosarcoma, accounting for 50-70% of cases . It is typically seen in children below the age of 15.
Pathology
Embryonal rhabdomyosarcomas are further divided into three sub types :
- spindle cell rhabdomyosarcoma
- resembles leiomyosarcoma
- good prognosis
- botryoid rhabdomyosarcoma
- anaplastic rhabdomyosarcoma
Location
Typically these tumors arise in the head and neck and genitourinary tract
- head and neck - 50%
- see rhabdomyosarcomas of the head and neck
- orbit
- middle ear
- nasal cavity and paranasal spaces
- pelvis - 30%
- see rhabdomyosarcomas of the genitourinary tract
- prostate
- paratesticular
- retroperitoneum
- extremities
Radiographic features
The features are non-specific (see radiographic features in the parent article: rhabdomyosarcoma), although, in general, embryonal rhabdomyosarcomas tend to be more homogeneous. When located in the extremities, they may cause bowing of long bones in children .
Siehe auch:
- Rhabdomyosarkom
- Leiomyosarkom
- Rhabdomyosarkom der Kopf-Hals-Region
- botryoid rhabdomyosarcoma
- anaplastic rhabdomyosarcoma
- Spindelzelliges Rhabdomyosarkom
und weiter:
Assoziationen und Differentialdiagnosen zu embryonales Rhabdomyosarkom:
