Fehlbildungen der Gehörknöchelchen

External and

middle ear diseases: radiological diagnosis based on clinical signs and symptoms. Congenital external ear malformation. Axial CT scan, bone window. Deformed ossicular chain is visible within hypoplastic tympanic cavity. Proper malleus and incus together with malleo-incudal joint can not be identified, instead, there is a V-shaped bony structure, representing the fused malleo-incudal complex

External and

middle ear diseases: radiological diagnosis based on clinical signs and symptoms. Severe external and middle ear deformity accompanying Goldenhar syndrome (oculoauricular dysplasia). Coronal CT scan shows, that tympanic bone, forming the floor of EAC is absent. It also results in temporomandibular joint incomplete formation

Pre- and

post-operative imaging of cochlear implants: a pictorial review. A 5-year-old male patient, with CHARGE syndrome and bilateral severe SNHL from birth. HRCT axial image shows hypoplastic cochlea type III with less than 2 turns (arrowhead). Malformed crus longum incudis and stapes are fused with the posterior tympanic wall (arrow)

Pre- and

post-operative imaging of cochlear implants: a pictorial review. A 1-year-old male patient, with sensorineural deafness from birth. HRCT axial image (left) and coronal image (right) show incomplete partition type I, with empty cystic cochlea (C) and a large dilated vestibulum (V). Stapes is malformed and fused with the incus (arrow)