kindlicher ossifizierender Nierentumor
Ossifying renal tumor of infancy (ORTI) is a rare renal tumor.
Epidemiology
- extremely rare, <<1% of pediatric renal neoplasms (17 cases reported)
- 6 days - 3 months
- male predominant
Pathology
Histology reveals spindle cells and osteoblastic cells in a calcified osteoid matrix. It is thought to originate from intralobar nephrogenic rests.
Radiographic features
Abdominal radiography
- often resembles a staghorn calculus
Ultrasound
- calcification is hyperechoic
- there may be intra-tumoral flow on color Doppler ultrasound
CT
ORTI may resemble a staghorn calculus since it originates from the renal papilla, but it enhances postcontrast.
Treatment and prognosis
Cases of ORTI so far have been benign, with no recurrence after resection.
Differential diagnosis
Siehe auch:
Assoziationen und Differentialdiagnosen zu kindlicher ossifizierender Nierentumor:
