lipoblastoma

School ager
with cough and fever. CXR PA and lateral (above) shows a right sided chest mass in the posterior mediastinum. Axial CT with contrast of the chest (below) shows a homogeneous mass, of fat density, with a few septations, in the right posterior mediastinum causing some anterior displacement of the right mainstem bronchus.The diagnosis was lipoblastoma in the posterior mediastinum.
pediatricimaging.org • CC-by-nc-sa 4.0
Cervicothoracic
lipoblastoma: three case reports and review of literature. a Neck mass with dilated superficial veins. b CXR tracheal deviation to the right side. c Lt neck mass with intrathoracic extension measuring about 7×8 cm. d The mass pushed upper mediastinum to the left. e, f The left subclavian artery was encapsulated by the fatty mass
aops.springeropen.com • CC-by-4.0
Cervicothoracic
lipoblastoma: three case reports and review of literature. a, b MRI. c The mass stretching of the brachial plexus (isolated in the vessel loops). d Removing cervical portion exposed the left subclavian vein (pointed to it by the Debakey forceps). e The subclavian artery (blue vessel loop), subclavian vein (lower vessel loop), and the brachial plexus (upper vessel loop) with empty cavity. f Histopathology
aops.springeropen.com • CC-by-4.0
Cervicothoracic
lipoblastoma: three case reports and review of literature. a, b Intrathoracic lipoblastoma remnant. c Follow-up CXR
aops.springeropen.com • CC-by-4.0
Cervicothoracic
lipoblastoma: three case reports and review of literature. a Mass delivered to wound. b 11×4×5.5 cm, smooth, lobular, yellow-tan mass, weighed 90 g. c CT neck and chest. d MRI neck and chest
aops.springeropen.com • CC-by-4.0
Radiopaedia • CC-by-nc-sa 3.0 • de

Lipoblastoma is a rare, benign, encapsulated tumor arising from embryonic white fat.

Epidemiology

It occurs primarily in infancy and early childhood (more than 90% before age 3 years).

Clinical presentation

May present as a rapidly enlarging mass . It most often occurs in the extremities and trunk, although it can be seen in other areas . The entity was originally described as an infiltrating anterior chest wall mass.

Pathology

Location
Classification

The WHO classification of tumors of soft tissue categorizes this entity under adipocytic tumors.

Radiographic features

Imaging features are non-specific. Lipoblastoma is classically a predominantly fatty mass with well-defined margins. However, it may have myxoid components that predominate and that can also be enhancing.

Treatment and prognosis

Lipoblastomas have traditionally been treated with excision, although this practice has been called into question. There is a recurrence rate of up to 20% with no recorded cases of metastasis. Some cases have matured into lipomas .

Differential diagnosis

Lipoblastomas can look very much like a liposarcoma, however liposarcoma is extremely rare in children (0.08% occur under age 10 years) .

Siehe auch:
und weiter:
Assoziationen und Differentialdiagnosen zu Lipoblastom:
Liposarkom
 
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