Metastasen bei Angiosarkom des Herzens
Unusual CT
features of primary cardiac metastatic angiosarcoma. Mediastinal lymphadenopathies (arrows) are observed.
Unusual CT
features of primary cardiac metastatic angiosarcoma. Multiple bilateral metastases (circles) are shown, many in sub-pleural topography.
Metastasen bei Angiosarkom des Herzens
Angiosarkom des Herzens Radiopaedia • CC-by-nc-sa 3.0 • de
Cardiac angiosarcomas are the most common sarcoma involving the heart (see cardiac tumors).
Please refer to the article on angiosarcomas for a general discussion about this entity.
Epidemiology
They occur slightly more frequently in males.
Clinical presentation
Patients usually present with right-sided heart failure or cardiac tamponade.
Pathology
These tumors tend to occur in the right atrium and involve the pericardium.
Radiographic features
Two main morphologic types have been described in angiosarcoma:
- CT shows a low-attenuation right atrial mass, which may be irregular or nodular (usually arises from the right atrial free wall)
- contrast material enhancement is heterogeneous
- pericardial space may be obliterated with hemorrhagic, necrotic tumor debris
Treatment and prognosis
Prognosis is poor, which may be due in part to the delay in diagnosis (patients usually have metastatic involvement at presentation).
Siehe auch:
Assoziationen und Differentialdiagnosen zu Metastasen bei Angiosarkom des Herzens: