Zinner-Syndrom

Congenital
seminal vesicle cyst in Zinner syndrome. The liver is shown. The right kidney is not seen in its usual location.
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Zinner
Syndrome. (a-c) showing multiple thin-walled hyperintense cystic lesions (star) and hyperintense tubular structure in the right side(arrow), (d) the lesion is hyperintense and doesn"t have fatty content.
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Zinner’s
syndrome, radiological diagnosis for a rare syndrome with non-specific clinical presentation: case report. Post-IV contrast axial (a) and coronal (b) CT images. The upper abdomen shows single left kidney with absent right kidney. Images in the pelvis showed a lobulated non-enhancing cystic lesion replacing the right seminal vesicle, inseparable from the right upper surface of the prostate and exerting mass effect upon the surrounding structures, upon which MRI was requested
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Zinner’s
syndrome, radiological diagnosis for a rare syndrome with non-specific clinical presentation: case report. US images of the pelvis showing a lobulated cystic lesion with rather clear contents and posterior enhancement arising from the right seminal vesicle measuring about 6 × 6 × 8 cm in its maximum dimensions and indenting the UB and prostate; otherwise, the normal sonographic appearance of the other pelvic structures including the left vesicle is preserved
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Congenital
seminal vesicle cyst in Zinner syndrome. CT with intravenous contrast demonstrating a hypodense homogeneous mass in the location described. It does not show contrast enhancement.
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Congenital
seminal vesicle cyst in Zinner syndrome. CT with coronal reformation showing absence of the right kidney and reduced size of the left kidney
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Congenital
seminal vesicle cyst in Zinner syndrome. CT with coronal reformation demonstrating the presence of a cyst in the right seminal vesicle abutting on the bladder wall
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Zinner
Syndrome. (a-b) showing retrovesical hypodense lesion with macrolobulated contour(star), and hypodense tubular structure was thought to be a remnant ureteric bud (arrow); absence of right kidney.
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Zinner
Syndrome. (a-c) showing multiple thin-walled hyperintense cystic lesions (star) and hyperintense tubular structure in the right side(arrow), (d) the lesion is hyperintense and doesn"t have fatty content.
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Zinner
Syndrome. (a-b) showing hyperintense lesion in b800 DWI and ADC map.
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Zinner
Syndrome. (a-c) showing multiple thin-walled hyperintense cystic lesions (star) and hyperintense tubular structure in the right side(arrow), (d) the lesion is hyperintense and doesn"t have fatty content.
www.eurorad.org • CC by-nc-sa-4.0
Congenital
seminal vesicle cyst in Zinner syndrome. An anechoic rounded image (arrow) is seen posterior to the bladder. It has contact with the right seminal vesicle which shows dilation (asterisk).
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Zinner
Syndrome. (a-c) showing multiple thin-walled hyperintense cystic lesions (star) and hyperintense tubular structure in the right side(arrow), (d) the lesion is hyperintense and doesn"t have fatty content.
www.eurorad.org • CC by-nc-sa-4.0
Zinner
Syndrome. (a-b) showing hyperintense lesion in b800 DWI and ADC map.
www.eurorad.org • CC by-nc-sa-4.0
Zinner
Syndrome. (a-b) showing retrovesical hypodense lesion with macrolobulated contour(star), and hypodense tubular structure was thought to be a remnant ureteric bud (arrow); absence of right kidney.
www.eurorad.org • CC by-nc-sa-4.0
Zinner’s
syndrome, radiological diagnosis for a rare syndrome with non-specific clinical presentation: case report. MRI images—axial T2 WIs (c–e), coronal T2 FS WIs (f), and post-contrast T1 fat sat axial image (g) showing a lobulated tubular fluid-filled cystic lesion replacing the right seminal vesicle with no contrast enhancement in the post-contrast images seen exerting mass effect upon the surrounding structures, while the left vesicle and prostate are seen of normal MRI appearance
ejrnm.springeropen.com • CC-by-4.0
Radiopaedia • CC-by-nc-sa 3.0 • de

Zinner syndrome is a triad of mesonephric (Wolffian) duct anomalies comprising unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ejaculatory duct obstruction .

Clinical presentation

Patients are typically diagnosed during the 3 or 4 decade of life and often present with perineal pain, recurrent prostatitis, hematospermia, painful ejaculation, and infertility.

Pathology

There is an association between congenital malformations of the seminal vesicle and the ipsilateral upper urinary tract because both the ureteral buds and the seminal vesicles originate from the mesonephric (Wolffian) duct .

Maldevelopment of the distal part of the mesonephric duct results in atresia of the ejaculatory duct (leading to obstruction and dilatation of the seminal vesicle), while an abnormality in the ureteral bud leads to renal agenesis/dysplasia .

Radiographic features

Irrespective of imaging modality, the key findings are:

Small testis and ipsilateral ureterocele have also been reported .

Treatment and prognosis

In asymptomatic patients, treatment is usually conservative, however, symptomatic patients are often treated surgically .

History and etymology

Zinner syndrome was first described by A Zinner in 1914 .

Differential diagnosis

Seminal vesicle cysts should be differentiated from other cysts such as :

See also

Siehe auch:
und weiter:
Assoziationen und Differentialdiagnosen zu Zinner-Syndrom:
einseitige
Nierenagenesie
Wikipedia • CC BY-SA 4.0
dilatierte
Samenbläschen mit multiplen Zysten
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