Chiari III malformation

Newborn with
an abnormal bump in the posterior midline at the skull base. Axial CT without contrast of the cervical spine shows a defect in the posterior skull at the craniocervical junction with cerebellar tissue herniating posteriorly through it.The diagnosis was Chiari III malformation with an occipital encephalocele.

Chiari III
malformation • Chiari III malformation - Ganzer Fall bei Radiopaedia

Chiari III
malformation • Chiari III malformation - repaired - Ganzer Fall bei Radiopaedia

Chiari III
malformation • Chiari III malformation with occipital encephalocele - Ganzer Fall bei Radiopaedia
Chiari III malformation is an extremely rare anomaly characterized by a low occipital and high cervical encephalocele with herniation of posterior fossa contents, that is, the cerebellum and/or the brainstem, occipital lobe, and fourth ventricle.
Pathology
Associations
- agenesis of the corpus callosum
- syringohydromyelia of the cervical cord
See also
Siehe auch:
und weiter:

