Scaphocephaly (also known as dolichocephaly) is the most common form of craniosynostosis, where premature closure of the sagittal suture results in an impediment to the lateral growth of the skull while anteroposterior growth continues, producing a narrow and elongated skull. Causes are primary, or secondary to certain hematologic disorders, metabolic disorders, bone dysplasias, and syndromes.
Scaphocephaly accounts for approximately 50% of all cases of craniosynostosis and has a male predilection with an M:F ratio of 3:1.
Treatment and prognosis
Treatment is often with a cranioplasty. In contrast to other craniosynostoses, there is near normal IQ and no hydrocephalus.
History and etymology
The term is derived from the Ancient Greek words "skaphe" meaning a light boat and "kephale" meaning head and describes an elongated head resembling an inverted boat.