Linsenluxation
Traumatische
Linsenluxationen rechts bei Zustand nach Linsenoperation bei grauem Star links. Auf der rechten Seite zeigt sich die Linse als rundliche, hyperdense Formation dorsal gelegen bei Fehlen der normalen anatomischen Augenlinse in der erwarteten Position. In der augenärztlichen Untersuchung zeigte sich dann zusätzlich auch eine Luxation der linksseitigen Kunst-Linse, welche jedoch CT-morphologisch nicht lokalisiert werden kann. Die normale, anatomische Augenlinse ist gegenüber den umgebenden Strukturen hyperdens. Ein Linsenersatz ist normalerweise zum Glaskörper isodens, weshalb die linksseitige Luxation der Kunst-Linse dem computertomografischen Nachweis entging.
Ectopia
lentis • Ectopia lentis - Ganzer Fall bei Radiopaedia
Subluxed
right lens post head injury with an incidental finding of a pseudophakic left eye. Demonstrating right eye lens subuxation and a pseudophakic left eye.
Ectopia
lentis • Traumatic lens dislocation - Ganzer Fall bei Radiopaedia
Incidental
finding of right lens dislocation following trauma. CT head in sagittal plane showing the right dislocated lens.
Incidental
finding of right lens dislocation following trauma. Axial CT head non-contrast at the level of the orbits showing a right medial lens dislocation
Ocular
ultrasonography focused on the posterior eye segment: what radiologists should know. Complete lens dislocation in a man with a history of ocular trauma. Axial US image shows the dislocated lens (arrow), which lies entirely within the vitreous. Membranes from associated vitreous haemorrhage can also be seen
Ocular
ultrasonography focused on the posterior eye segment: what radiologists should know. Partial lens dislocation in a 45-year-old man with a history of ocular trauma 2 years earlier. He developed a post-traumatic cataract, and physical examination detected an abnormal vibration or agitated motion of the iris during eye movements—the so-called iridodonesis (movie 1). a US examination with the patient in a supine position showed a globulous lens situated in a normal position, as well as cataracts. b US examination with the patient sitting upright revealed that the lens was detached at the 12 o’clock position. It is sometimes useful to perform US studies with the patient in different positions
Ectopia
lentis • Ectopia lentis - Ganzer Fall bei Radiopaedia
Ectopia
lentis • Traumatic lens dislocation - Ganzer Fall bei Radiopaedia
Ectopia
lentis • Lens dislocation - Ganzer Fall bei Radiopaedia
Ectopia
lentis • Ectopia lentis - Ganzer Fall bei Radiopaedia
Subluxed
right lens post head injury with an incidental finding of a pseudophakic left eye. Demonstrating right eye lens subluxation.
Ectopia
lentis • Ectopia lentis - Ganzer Fall bei Radiopaedia
Ectopia
lentis • Lens dislocation - Ganzer Fall bei Radiopaedia
Ectopia
lentis • Ectopia lentis - Ganzer Fall bei Radiopaedia
Traumatic
lens dislocation. CT image corresponding to point-of-care ultrasound showing dislocated lens (white arrow)
Traumatic
lens dislocation. Sagittal view of left eye globe showing floating lens in the posterior chamber (white arrow)
Ectopia
lentis • Homocystinuria presenting as cerebral venous thrombosis - Ganzer Fall bei Radiopaedia
Ectopia lentis refers to subluxation or dislocation of the lens of the eye secondary to dysfunction or disruption of zonular fibers. It is most commonly due to trauma. The commonest atraumatic etiologies are Marfan syndrome and homocystinuria.
Pathology
Etiology
- trauma
- systemic and syndromic disorders
- Marfan syndrome
- typically upwards and out
- most common spontaneous cause
- homocystinuria - typically downwards
- Weil-Marchesani syndrome
- Ehlers-Danlos syndrome
- Marfan syndrome
- hereditary (or isolated) ectopia lentis
- primary ocular disorders
- aniridia
- intraocular tumors
- infective conditions, e.g. syphilis
Marfan syndrome, homocystinuria and Weil-Marchesani syndrome account for the vast majority of non-traumatic cases.
Radiographic features
Ultrasound
Sonographic features of lens malposition differ based upon the degree of luxation as follows :
- subluxation
- unilateral deviation of the lens margin posteriorly into the anechoic vitreous body
- the contralateral margin remains fixed adjacent to the iris
- complete luxation
- the lens assumes a dependent position in the vitreous
- demonstrates free mobility with eye movements
Associated findings include:
- traumatic cataract
- increased echogenicity of the lens is suggestive
- vitreous hemorrhage
Treatment and prognosis
Complications
An anterior dislocation/subluxation carries greater complications than a posterior one. Such complications include:
- acute glaucoma
- corneal injury
- iridal injury
Siehe auch:
- Ehlers-Danlos syndrome
- Glaskörperblutung
- Pseudoexfoliationssyndrom
- traumatic crystalline lens dislocation
- künstliche Augenlinse
und weiter:
Assoziationen und Differentialdiagnosen zu Linsenluxation: