muskuloskelettale Fibromatose

Musculoskeletal fibromatoses represent a wide spectrum of fibroblastic and myofibroblastic neoplasms with similar pathologic appearances and variable clinical behavior.

Pathology

They are benign fibrous tissue proliferations characterized by infiltrative growth and a tendency for local recurrence without metastasis .

Classification

These lesions can be variably categorized by location (superficial or deep) or by the age group predominantly affected. One method is as

• superficial fibromatoses (fascial)
  • adults
    • palmar fibromatosis - Dupuytren's disease
    • plantar fibromatosis - Ledderhose's disease
    • knuckle pads
  • children / infants
    • calcifying aponeurotic fibroma / juvenile aponeurotic fibroma
    • lipofibromatosis
    • infantile digital fibroma
    • inclusion body fibromatosis
• deep fibromatoses (musculoaponeurotic)
  • adults 
    • desmoid-type fibromatoses
      • desmoid tumor
        • intra-abdominal desmoid tumors
          • mesenteric desmoid tumor
          • pelvic fibromatosis
        • abdominal wall fibromatosis
        • extra-abdominal desmoid tumors
          • extra-abdominal desmoid tumor of the breast
          • well-differentiated nonmetastasising fibrosarcoma
          • aggressive fibromatosis
  • children
    • fibromatosis colli
    • myofibroma
    • myofibromatosis / infantile myofibromatosis / aggressive infantile fibromatosis

See also

• WHO 2002 classification of soft tissue tumors

Siehe auch:

• Fibromatosis colli
• WHO Klassifikation der Weichteiltumoren
• Morbus Ledderhose
• Fibromatose der Mamma
• Morbus Dupuytren
• Desmoid-Tumor - aggressive Fibromatose
• Desmoid-Tumor des Mesenteriums

und weiter:

• Fibromatose
• extrabdominale Fibromatosen