Trigonocephalie
Infant with a
pointy head. Axial CT without contrast of the brain (left) shows fusion of the metopic suture in the midline and a triangular appearance to the anterior aspect of the skull (trigonocephaly). Anterior 3D CT reconstruction (right) shows a prominent midline ridge in the anterior skull and hypotelorism with quizzical eye deformities present bilaterally.The diagnosis was metopic suture craniosynostosis.
Infant with a
bump on the forehead. Axial CT without contrast of the brain (left) shows fusion of the metopic suture in the midline and a triangular appearance to the anterior aspect of the skull (trigonocephaly). Anterior 3D CT reconstruction (right) shows a prominent midline ridge in the anterior skull and hypotelorism with quizzical eye deformities present bilaterally.The diagnosis was metopic suture craniosynostosis.
Trigonocephaly refers to the triangular appearance of the frontal skull created by premature fusion of the metopic suture (metopic craniosynostosis) . Trigonocephaly accounts for around 5% of all craniosynostosis cases.
Pathology
The metopic suture divides the frontal bones in the midline. It begins at the nose and continues superiorly to meet the sagittal suture. The metopic suture is usually open at birth and normally fuses in the first 12 months of life. Premature fusion prevents transverse growth of the forehead which causes a triangular shaped forehead that may be associated with orbital hypotelorism (abnormal closeness of the eyes) .
Associations
Siehe auch:
Assoziationen und Differentialdiagnosen zu Trigonocephalie:
