Carney-Trias
Carney triad
(ECR 2016 Case of the Day). Chest CT scan shows bilateral calcified lung nodules suggesting pulmonary chondromas.
Carney triad
(ECR 2016 Case of the Day). Follow-up CT 6 years later shows further calcification and enlargement of prior lung lesions, as well as appearance of a new nodule in the left lower lobe (arrow).
Carney triad
(ECR 2016 Case of the Day). Coronal CT image shows same findings. These lesions should not be confused with calcified metastases.
Carney triad
(ECR 2016 Case of the Day). Chest CT shows nodule in the aortopulmonary window with intense contrast enhancement.
Carney triad
(ECR 2016 Case of the Day). Octreotide scan was performed for suspicion of aortopulmonary paraganglioma, demonstrating intense uptake.
Carney triad
(ECR 2016 Case of the Day). Coronal CT image shows exophytic mass from the medial aspect of the gastric fundus.
nicht verwechseln mit: Carney triad is a rare syndrome defined by the coexistence of three tumors:
- extra-adrenal paraganglioma (e.g. spinal paraganglioma)
- initially, only functioning extra-adrenal paragangliomas were included, but subsequent work includes non-functioning extra-adrenal paragangliomas
- gastric gastrointestinal stromal tumors (GIST)
- pulmonary chondroma
In most cases, only 2 of the 3 tumors are present at the time of diagnosis. It typically affects young people.
Terminology
It is not to be confused with the related Carney-Stratakis syndrome, or the unrelated Carney complex
History and etymology
First described by J Aidan Carney, an American professor of pathology, and colleagues in 1977 .
Siehe auch:
- Paragangliom
- Phäochromozytom
- gastrointestinaler Stromatumor des Magens
- Carney-Komplex
- pulmonale Chondrome
und weiter:
Assoziationen und Differentialdiagnosen zu Carney-Trias:
