Pulmonary hypertension (2013 classification)

ähnliche Suchen

Pulmonary hypertension (2013 classification)
Fifth world symposium on pulmonary hypertension classification
Fifth world symposium on pulmonary arterial hypertension classification
Fifth world symposium on PAH classification
Pulmonary arterial hypertension (2013 classification)
Nice classification of pulmonary hypertension

In 2013, the 5 World Symposium on pulmonary hypertension took place in Nice, France and modified the classification system for pulmonary hypertension.

The modified system divides pulmonary hypertension into five groups:

• group 1: pulmonary arterial hypertension (disorders of the pulmonary arteries themselves)
  • 1.1: idiopathic pulmonary arterial hypertension
  • 1.2: heritable pulmonary hypertension
  • 1.3: drug- and toxin-induced pulmonary hypertension
  • 1.4: pulmonary hypertension associated with 
    • connective tissue disease
    • HIV infection - HIV-associated pulmonary arterial hypertension
    • portal hypertension
    • congenital heart disease
    • schistosomiasis
• group 2: pulmonary hypertension due to left-sided heart disease
  • 2.1: systolic dysfunction
  • 2.2: diastolic dysfunction
  • 2.3: valvular disease
  • 2.4: congenital/acquired left heart inflow/outflow tract obstruction and congenital cardiomyopathies
• group 3: pulmonary hypertension due to lung diseases and/or hypoxia
  • chronic obstructive pulmonary disease
  • interstitial lung disease
  • other pulmonary diseases with mixed restrictive and obstructive pattern
  • sleep-disordered breathing
  • alveolar hypoventilation disorders
  • chronic exposure to high altitude
  • developmental lung disease 
• group 4: pulmonary hypertension due to chronic pulmonary thromboembolism
• group 5: pulmonary hypertension due to unclear multifactorial mechanisms
  • hematologic disorders
    • chronic hemolytic anemia
    • myeloproliferative disorders
    • splenectomy
  • systemic disorders
    • sarcoidosis
    • pulmonary histiocytosis
    • lymphangioleiomyomatosis
  • metabolic disorders
    • glycogen-storage disease
    • Gaucher disease
    • thyroid disorders
  • other conditions
    • fibrosing mediastinitis
    • tumoral obstruction
    • chronic renal failure
    • segmental pulmonary hypertension