primary retroperitoneal neoplasms

Computertomographie
ohne und mit Kontrastmittel eines großen retroperitonealen solitären fibrösen Tumors.
Wikipedia • CC BY 3.0
Imaging of
incidentally discovered ossifying fibromyxoid tumour of retroperitonuem with histopathological correlation: a rare case report. Contrast-enhanced arterial phase axial CT image further below pedicle-shaped attachment of the lesion to ipsilateral psoas muscle.
www.eurorad.org • CC by-nc-sa-4.0
Primary
retroperitoneal neoplasms • Undifferentiated pleomorphic sarcoma of the retroperitoneum - Ganzer Fall bei Radiopaedia
Glick Y, Undifferentiated pleomorphic sarcoma of the retroperitoneum. Case study, Radiopaedia.org (Accessed on 06 Oct 2023) https://doi.org/10.53347/rID-172448 • CC by-nc-sa 3.0 (modified)
Primary
retroperitoneal neoplasms • Malignant peripheral nerve sheath tumor - Ganzer Fall bei Radiopaedia
Ibrahim D, Malignant peripheral nerve sheath tumor. Case study, Radiopaedia.org (Accessed on 23 Jan 2023) https://doi.org/10.53347/rID-32454 • CC by-nc-sa 3.0 (modified)
Primary
retroperitoneal neoplasms • Retroperitoneal soft tissue sarcoma - Ganzer Fall bei Radiopaedia
Alshammari M, Retroperitoneal soft tissue sarcoma. Case study, Radiopaedia.org (Accessed on 23 Jan 2023) https://doi.org/10.53347/rID-16248 • CC by-nc-sa 3.0 (modified)
Imaging of
incidentally discovered ossifying fibromyxoid tumour of retroperitonuem with histopathological correlation: a rare case report. Contrast-enhanced arterial phase axial CT image of the abdomen shows a well-defined moderately enhancing lesion in the left para-aortic region seen closely abutting the left psoas muscle.
www.eurorad.org • CC by-nc-sa-4.0
Magnetresonanztomographie
T1- und T2-gewichtet eines großen retroperitonealen solitären fibrösen Tumors.
Wikipedia • CC BY 3.0
Retroperitoneal
haemorrhagic cystic lymphangioma. Axial non-enhanced abdominal CT. Arrow: Bleeding area.
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Retroperitoneal
haemorrhagic cystic lymphangioma. Sagittal contrast-enhanced abdominal CT. Cyst mass pushes the transverse colon (arrow).
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Retroperitoneal
haemorrhagic cystic lymphangioma. Axial contrast-enhanced abdominal CT. Fluid in left iliac fossa (arrow) and inside the Douglas’ pouch (arrowhead).
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Retroperitoneal
haemorrhagic cystic lymphangioma. MIP Axial contrast-enhanced abdominal CT. Cyst mass including splenic vessels (arrow).
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Retroperitoneal
haemorrhagic cystic lymphangioma. Coronal contrast-enhanced abdominal CT. Extensive cyst mass in the left hemiabdomen.
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Retroperitoneal
haemorrhagic cystic lymphangioma. Oblique slice on the left hypochondrium and left lumbar region. Arrow: Membranes inside the cyst. K: Kidney.
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Management of
a giant retroperitoneal leiomyoma: a case report. A retroperitoneal tumor with a mass effect on the left kidney, the aorta, and the bowel. 1 = Tumor, 2 = left kidney, 3 = aorta, 4 = left kidney artery, 5 = iliac artery, 6 = pancreas
jmedicalcasereports.biomedcentral.com • CC-by-4.0
Radiopaedia • CC-by-nc-sa 3.0 • de

Primary retroperitoneal neoplasms are an extremely rare group of tumors (lymphoma is not included in this definition). The most common type is soft tissue sarcoma (90%).

Epidemiology

The most common age for presentation is 40-50 years.

Clinical presentation

Frequently tumors have relatively unimpeded growth where symptoms develop late and the tumor at presentation tending to be extremely large (average size 11-20 cm).

Pathology

Primary retroperitoneal neoplasms arise from outside the major organs, and are divided according to histological types:

  • mesenchymal origin: skeletal muscle, fat, peripheral nerve, vessels, fibrous tissue
  • extragonadal germ cell tumors
  • primary retroperitoneal adenocarcinoma
Etiology

The order of frequency of primary retroperitoneal malignancy is as follows:

Causes include radiotherapy, e.g. neuroblastoma treatment as a child.

Radiographic features

Imaging is used to confirm the diagnosis, assess for any metastatic disease and determine the potential for resection. CT is the most commonly used tool. MRI can be used for further differentiation, but histology is always required.

Percutaneous biopsy may be undertaken (after consultation with surgeons and oncologists), and for assessment of tumor grade, PET may be used .

Treatment and prognosis

Prognosis depends on the histological type of a tumor and the potential for resection.

Recurrence rates are high (90% in some series), so imaging surveillance is an important part of continued follow-up.

See also

Siehe auch:
und weiter:
Assoziationen und Differentialdiagnosen zu retroperitoneale Tumoren:
maligner
peripherer Nervenscheidentumor (MPNST)
Wikipedia • CC BY-SA 3.0
retroperitoneale
Sarkome
www.eurorad.org • CC by-nc-sa-4.0
pleomorphes
undifferenziertes Sarkom des Retroperitoneums
www.eurorad.org • CC by-nc-sa-4.0
retroperitoneales
Hamartom
bmcgastroenterol.biomedcentral.com • CC-by-4.0
solitärer
fibröser Tumor des Retroperitoneums
Wikipedia • CC BY 3.0
retroperitoneale
Metastasen
Wikipedia • CC BY-SA 4.0
retroperitoneales
Leiomyom
jmedicalcasereports.biomedcentral.com • CC-by-4.0
retroperitoneales
Ganglioneurom
www.eurorad.org • CC by-nc-sa-4.0