Fehlbildungen der Gebärmutter

Uterus
bicornis bicollis mit gemeinsamer Portioöffnung: Das Cavum uteri ist vollständig getrennt, es gibt aber noch gemeinsames Myometrium (sonst Uterus didelphys); Septum in nahezu der kompletten Zervix. MRT T2, links 2 Schichten paracoronar, rechts 3 Schichten axial in verschiedenen Höhen.

Uterus
subseptus in der Computertomographie links axial und rechts in der Ebene des Uterus rekonstruiert. Zusätzlich zystischer Tumor mit abgebildet.

Accessory and
cavitated uterine mass (ACUM)- A rare Mullerian anomaly. STIR axial image showing thick-walled lesion contiguous with the left lateral uterine wall.

Accessory and
cavitated uterine mass (ACUM)- A rare Mullerian anomaly. T1 fat suppressed axial image shows bright signal in the central part of the lesion consistent with signal intensity of blood degradation products.
There are many classification systems for congenital utero-vaginal anomalies. These include:
- Buttram and Gibbons classification
- American Fertility Society (AFS) classification
- Modified Rock and Adam - AFS classification
Modified Rock and Adam - AFS classification
This classification divides congenital uterine anomalies into four main types:
- class I: dysgenesis of Müllerian ducts
- includes agenesis or hypoplasia of the müllerian duct derivatives: the uterus and upper two-thirds of the vagina
- the most common form is the Mayer-Rokitansky-Kuster-Hauser syndrome which is the combined agenesis of the uterus, cervix, and upper portion of the vagina
- class II: disorders of vertical fusion
- these anomalies are due to failure of fusion of the müllerian system with the sinovaginal bulb
- they include cervical dysgenesis and obstructive and nonobstructive transverse vaginal septa
- class III: disorders of lateral fusion
- describes anomalies that result in a duplicated or partially duplicated reproductive tract
- these disorders are due to impaired fusion and/or septal resorption of fusing Müllerian ducts attempting to form the uterus, cervix, and upper vagina
- it includes anomalies due to failure of fusion of the paired müllerian ducts (as in didelphic and bicornuate uteri) and failure of midline septum resorption after fusion (as in septate uterus)
- disorders due to lateral fusion defects are further subclassified into
- a: symmetric non-obstructive forms seen in five types: unicornuate, bicornuate, didelphic, septate, and DES-related uteri
- b: asymmetric obstructive forms seen in three types: unicornuate uterus with obstructed horn, double uterus with unilaterally obstructed horn, and double uterus with unilaterally obstructed vagina
- class IV: unusual configurations and combinations of defects
Siehe auch:
- Uterus
- Uterus didelphys
- Müllerian duct anomaly classification
- uterine agenesis
- Mayer-Rokitansky-Küster-Hauser syndrome
- Müller-Gang
- Uterus bicornis
- transverses Vaginalseptum
- Uterus septus
- Uterus arcuatus
- uterine duplicational anomalies
- Vaginalseptum
- Müller-Gang-Persistenzsyndrom
- class IV Mullerian duct anomaly
- obstruierte Hemivagina und ipsilaterale renale Anomalie (OHVIRA) Syndrom
- Uterus unicornis
und weiter:
