Hemihyperplasie
Hemihyperplasia.
Dilated bowel loops, consistent with small bowel obstruction (due to adhesions). Left nephrectomy. Obvious asymmetry in subcutaneous fat and abdominal wall muscles.
Hemihyperplasia.
Asymmetry also visible in lower thorax, with marked hyperplasia of the right side.
Hemihyperplasia.
Dilated small bowel loops with air-fluid levels. Hemihyperplasia is evident in the pelvis, with clear asymmetry of the iliac crests.
Hemihyperplasia.
Obvious hemihyperplasia of the trunk, especially evident in the breasts.
Hemihyperplasia
• Hemihyperplasia - Ganzer Fall bei Radiopaedia
Hemihyperplasia, also known as hemihypertrophy, is asymmetry in size between the right and left of the body, more than can be attributed to normal variation.
Terminology
Hemihyperplasia is more scientifically correct than hemihypertrophy as the cells are hyperplastic rather than hypertrophied .
Epidemiology
Incidence is estimated at 1 in ~50,000 live births .
Pathology
Etiology
Hemihyperplasia can arise sporadically as isolated hemihyperplasia, or it can arise as part of a syndrome :
- Beckwith-Wiedemann syndrome
- Proteus syndrome
- Klippel-Trénaunay syndrome
- neurofibromatosis type 1
- Hemihyperplasia-multiple lipomatosis (HHML)
- McCune Albright Syndrome
- Langer Giedion syndrome
Associations
Increased risk (5% of patients) of malignancy, most commonly Wilms tumors .
Differential diagnosis
- hemiatrophy
Siehe auch:
- Neurofibromatose Typ 1
- Poland-Syndrom
- Beckwith-Wiedemann-Syndrom
- Proteus-Syndrom
- Klippel-Trénaunay-Weber-Syndrom
- McCune-Albright Syndrom
- Neurofibromatose
- Tricho-rhino-phalangeale Dysplasie
- Russell-Silver syndrome
- Friedreich-Auerbach-Syndrom
- limb hypertrophy
- Hyperplasie
- primäre intestinale Lymphangiektasie
- lokaler Gigantismus
- Hemihyperplasie - multiple Lipomatosen Syndrom
und weiter:
Assoziationen und Differentialdiagnosen zu Hemihyperplasie:
