maligner rhabdoider Tumor

Extraordinary
disease-free survival in a rare malignant extrarenal rhabdoid tumor: a case report and review of the literature. Computed tomography scan describing a mass involving cecum and ascending colon (a) and the absence of recurrence at a 4-year follow-up (b)
jmedicalcasereports.biomedcentral.com • CC-by-4.0
Malignant
rhabdoid tumor of the liver in a middle-aged woman: a case report and literature review. (2019-02-15) Abdominal MRI: an irregular mass with mixed short T1-weighted imaging (T1WI), mixed long T2-weighted imaging (T2WI) and high diffusion-weighted imaging (DWI) under the capsule of the right lobe of the liver. After enhancement, the mass showed uneven enhancement. (1A: T1WI sequence; 1B: T2WI sequence; 1C: DWI sequence; 2A: Arterial phase; 2B: Portal phase; 2C: venous phase; 2D: delayed phase.)
bmcgastroenterol.biomedcentral.com • CC-by-4.0
Malignant
rhabdoid tumor of the liver in a middle-aged woman: a case report and literature review. (2019-06-24) Abdominal enhanced-CT: multiple heterogeneous dense masses with regular morphology and clear boundaries between the right lobe of liver and the diaphragm. The largest one was about 13.4 × 9.2 cm and the CT value was between 20-45Hu with no obvious enhancement on enhanced scans. (1A: Axial arterial phase; 1B: Coronary arterial phase; 1C: Sagittal arterial phase; 2A: Axial portal phase; 2B: Coronary portal phase; 2C: Sagittal portal phase; 3A: Axial delayed phase; 3B: Coronary delayed phase; 3C: Sagittal delayed phase.)
bmcgastroenterol.biomedcentral.com • CC-by-4.0
Rhabdoid
renal tumor: an aggressive embryonal tumor in an infant — a case report. Ultrasound picture: revealing a 7 cm heterogeneous spherical mass arising from the apical pole of the right kidney with multiple hemorrhagic areas and fine calcifications
aops.springeropen.com • CC-by-4.0
Rhabdoid
renal tumor: an aggressive embryonal tumor in an infant — a case report. A CT scan: revealing an important uretero-pyelo-calicielle dilation with fine calcifications
aops.springeropen.com • CC-by-4.0
Malignant
rhabdoid tumor in the renal allograft of an adult transplant recipient: a unique case of a rare tumor. Computed tomography (CT) scan revealed that both original kidneys exhibited atrophy (a, white arrows) and a large mass (a and b, triangle) measuring 7.4 × 6.3 × 6.0 cm with a mixed density in the upper pole of the inner transplanted kidney (a and b, black arrows). c. Macroscopic features of MRT of the transplanted kidney. The cut surface of the mass was white to grayish (arrow)
diagnosticpathology.biomedcentral.com • CC-by-4.0
Clinical and
prognostic analysis of 42 children with malignant rhabdoid tumor of the kidney: a 7-year retrospective multi-center study. Typical radiological and histopathological changes in children with MRTK. CT scan of the abdomen shows “crescent-shaped” fluid dark area(red arrow) (A-B).The histopathological findings were microscopic vacuolar nuclei, central eosinophilic nucleoli and intracytoplasmic eosinophilic inclusions.(HE 400×)(C),Typical microscopic changes can be seen after magnification(D)
bmcpediatr.biomedcentral.com • CC-by-4.0
Omental
rhabdomyosarcoma (primary rhabdoid tumor of greater omentum): a rare case report. Showing a large well defined mass of 9.8 × 7.4 cms along with displacement of the bowel loops
surgicalcasereports.springeropen.com • CC-by-4.0
Atypical
teratoid/rhabdoid tumor • Atypical teratoid rhabdoid tumor (AT/RT) - Ganzer Fall bei Radiopaedia
Dixon, A. Atypical teratoid rhabdoid tumor (AT/RT). Case study, Radiopaedia.org. (accessed on 07 Nov 2022) https://doi.org/10.53347/rID-10515 • CC by-nc-sa 3.0 (modified)
Radiopaedia • CC-by-nc-sa 3.0 • de

Rhabdoid tumors are rare and extremely aggressive tumors of early childhood. They occur in a number of locations:

This article touches on the generalities of these tumors, but each is then discussed separately.

Epidemiology

Almost all reported cases of rhabdoid tumors, regardless of site of origin, occur in young children, between birth and 2 years of age .

In approximately 10% of cases of renal malignant rhabdoid tumors, patients then subsequently develop intracranial atypical teratoid/rhabdoid tumor (AT/RT) .

Pathology

Irrespective of site of origin, rhabdoid tumors share deletions in the long arm of chromosome 22, mapped to the INI1 gene, believed to be a tumor suppressor .

These tumors contain characteristic rhabdoid cells, so-called on account of the light microscopy resemblance to skeletal muscle cells .

Siehe auch:
und weiter:
Assoziationen und Differentialdiagnosen zu maligner rhabdoider Tumor:
Rhabdomyosarkom
 
pediatricimaging.org • CC-by-nc-sa 4.0
Nephroblastom
 
pediatricimaging.org • CC-by-nc-sa 4.0
pädiatrische
Nierentumoren
pediatricimaging.org • CC-by-nc-sa 4.0
atypischer
teratoider rhabdoider Tumor
pediatricimaging.org • CC-by-nc-sa 4.0
maligner
rhabdoider Tumor der Niere
aops.springeropen.com • CC-by-4.0