carney triad


Carney triad is a rare syndrome defined by the coexistence of three tumors:
- extra-adrenal paraganglioma (e.g. spinal paraganglioma)
- initially, only functioning extra-adrenal paragangliomas were included, but subsequent work includes non-functioning extra-adrenal paragangliomas
- gastric gastrointestinal stromal tumors (GIST)
- pulmonary chondroma
In most cases, only 2 of the 3 tumors are present at the time of diagnosis. It typically affects young people.
Terminology
It is not to be confused with the related Carney-Stratakis syndrome, or the unrelated Carney complex
History and etymology
First described by J Aidan Carney, an American professor of pathology, and colleagues in 1977 .
Siehe auch:
- Paragangliom
- Phäochromozytom
- gastrointestinaler Stromatumor des Magens
- Carney-Komplex
- pulmonale Chondrome
und weiter:
