Lungenfibrose
Variables
Immundefektsyndrom (CVID) mit rezidivierenden Pneumonien und zunehmender Fibrose der Lunge.
Clinical and
radiological features of lung disorders related to connective-tissue diseases: a pictorial essay. Coronal multiplanar reformatted images. A, B demonstrate the presence of straight-edge sign in female RA patients showing interstitial lung fibrosis. This sign consists of a more pronounced fibrosis in the lung bases—with sharp demarcation in the cranio-caudal plane (white arrows in A, B)
Hermansky-Pudlak
syndrome-associated pneumothorax with rapid progression of respiratory failure: a case report. a Chest X-ray at the first visit of the patient to our hospital. Chest high-resolution computed tomography (HRCT) findings in the b upper and c lower lung fields at the first visit to our hospital. d Chest X-ray 2 years after the first visit to our hospital. Chest HRCT findings in the e upper and f lower lung fields 2 years after the first visit to our hospital
Pulmonary
fibrosis • Pulmonary fibrosis - UIP pattern - Ganzer Fall bei Radiopaedia
Pulmonary
fibrosis • Pulmonary fibrosis - Ganzer Fall bei Radiopaedia
Pulmonary
fibrosis • Pulmonary fibrosis - early - Ganzer Fall bei Radiopaedia
Pulmonary
fibrosis • Pulmonary fibrosis (severe) - Ganzer Fall bei Radiopaedia
Pulmonary
fibrosis • Pulmonary sarcoidosis - end-stage - Ganzer Fall bei Radiopaedia
Pulmonary
fibrosis • Pulmonary fibrosis (moderate severity) - Ganzer Fall bei Radiopaedia
Pulmonary
fibrosis • Pulmonary fibrosis - UIP pattern - Ganzer Fall bei Radiopaedia
Pulmonary
fibrosis • Early stage pulmonary fibrosis - Ganzer Fall bei Radiopaedia
An industrial
worker with shortness of breath. Large bilateral opacities with irregular margins in bilateral upper and mid lobes. Mediastinum - Multiple enlarged lymph nodes with egg shell calcification in the pre and paratracheal, prevascular, subcarinal regions and bilateral hila.
An industrial
worker with shortness of breath. Remaining lung shows groung glass opacities, interstitial thickening and cystic areas. There is volume loss in bilateral lungs.
Pulmonary or interstitial fibrosis is a descriptive term given when there is an excess of fibrotic tissue in the lung. It can occur in a wide range of clinical settings and can be precipitated by a multitude of causes.
Terminology
The term should not be confused with idiopathic pulmonary fibrosis, which is a progressive fibrotic lung disease.
Pathology
Fibrosis in the lung is a process that occurs in the interstitium. Pulmonary fibrosis can be localized, segmental, lobar, or affect the entirety of the lung(s). Among the many conditions associated with pulmonary fibrosis are:
- significant acute insult to the lungs
- adult respiratory distress syndrome
- from a significant pulmonary infection
- diffuse alveolar damage from any source
- inhaled substances
- coal/silica: progressive massive fibrosis
- asbestos: asbestos-related pulmonary fibrosis
- radiation: radiation-induced pulmonary fibrosis
- congenital conditions
- autoimmune conditions
- connective tissue disorders
- granulomatous conditions
- sarcoidosis: pulmonary manifestations of sarcoidosis
- tuberculosis: pulmonary manifestations of tuberculosis
- granulomatosis with polyangiitis: pulmonary manifestations of granulomatosis with polyangiitis
- others
- airway-centered interstitial fibrosis
- chronic conditions
- polymyalgia rheumatica (occasional case reports )
- medications: drug-induced lung disease
- combined pulmonary fibrosis and emphysema'
- aging
- some studies report thin-section CT findings associated with interstitial lung disease to some degree are frequently seen in "asymptomatic" elderly individuals
Radiographic features
CT
There are many features that can imply underlying pulmonary fibrosis, these include:
- honeycombing
- traction bronchiectasis
- lung architectural distortion
- reticulation
- interlobular septal thickening: this feature is not specific for fibrosis
See also
Siehe auch:
- pulmonale Tuberkulose
- Honigwabenmuster
- acute respiratory distress syndrome (ARDS)
- verdickte interlobuläre Septen
- pulmonale und mediastinale Sarcoidose
- zystische Fibrose
- chronic eosinophilic pneumonia
- retikuläres Muster
- combined pulmonary fibrosis and emphysema
- idiopathische Lungenfibrose
- Traktionsbronchiektasen
- chronic hypersensitivity pneumonitis
- progressive massive Fibrose
- Hermansky-Pudlak-Syndrom
- asbestos related pulmonary fibrosis
- pulmonary manifestations of granulomatosis with polyangitis
- medikamenteninduzierte Pneumonitis
- radiation induced pulmonary fibrosis
- mnemonic for upper lobe pulmonary fibrosis
- diffuser Alveolarschaden
und weiter:
- Sarkoidose
- Silikose
- causes of pulmonary arterial hypertension
- radiation-induced pulmonary fibrosis
- Sklerosiphonie
- Parenchymband
- Medulläres Schilddrüsenkarzinom
- What Every Radiologist Should Know about Idiopathic Interstitial Pneumonias
- giant cell interstitial pneumonia
- Silzbach sarcoidosis chest radiographic staging system
- cryptogenic fibrosing alveolitis
- radiation fibrosis of the lung (Pneumonitis)
- Lungengerüstvergröberung
- diffuse Alveolarblutung
- Fibrose UIP
- Amiodaronlunge
- pulmonale fibrotische Bänder
Assoziationen und Differentialdiagnosen zu Lungenfibrose: