microtia
![](https://pacs.de/sites/default/files/pictures/thumbs/data.pacs.de/1/1/2/0/0/8/40ec258f65b01ed5bc7dd7f52837454f6077bf55e4200575ed7d5dd3ab8e3808_big_gallery_thumb.jpg)
Microtia •
Microtia - Ganzer Fall bei Radiopaedia
![](https://pacs.de/sites/default/files/pictures/thumbs/data.pacs.de/1/1/2/0/0/9/c41f353227834e0a92c60d33879ae8_big_gallery_thumb.jpg)
Microtia •
Microtia: grade III - Ganzer Fall bei Radiopaedia
![](https://pacs.de/sites/default/files/pictures/thumbs/data.pacs.de/1/1/2/0/1/0/ef431c549d4910ab4d47ef1b2bfd90_big_gallery_thumb.jpg)
Microtia •
External auditory canal atresia - Ganzer Fall bei Radiopaedia
![](https://pacs.de/sites/default/files/pictures/thumbs/data.pacs.de/1/0/4/7/6/0/0._big_gallery_thumb.jpg)
Fetal
hydrocephalus • Craniofacial malformations (antenatal ultrasound) - Ganzer Fall bei Radiopaedia
Microtia refers to a small pinna of the ear, when is it completely absent it is termed anotia.
Epidemiology
The estimated incidence at around 1:9000 live births. It is more common in males and there is a recognized right sided predilection.
Pathology
Associations
Microtia can be associated with a wide spectrum of inner and middle ear anomalies . Isolated microtia is relatively uncommon. The most frequent associations include:
- ossicular dysplasia
- external auditory canal stenosis
- external auditory canal atresia
Wider organ associations include:
- renal anomalies
Syndromic associations include:
Classification
It is classified into four grades based on increasing severity:
- grade I: slightly small ear with identifiable structures; external auditory canal small but present
- grade II: partial or hemiear with a occluded or stenotic external ear canal producing a conductive hearing loss
- grade III: absence of the external ear with a small peanut like vestige structure and an absence of the external ear canal and eardrum
- grade IV: complete absence (anotia)
Siehe auch:
- Down-Syndrom
- einseitige Nierenagenesie
- Franceschetti-Zwahlen-Syndrom
- Goldenhar-Gorlin-Syndrom
- Gehörgangsatresie
- Jacobsen syndrome
- OFM Nager-Syndrom
- cross-fused ectopia
und weiter:
![Click für weniger anzeigen](/sites/all/modules/pacs/tools/imgs/collapse_up.png)
![](/sites/all/modules/pacs/tools/imgs/Iris_color_40.png)